Successful staged surgical repair of a rare association of cardiac rhabdomyoma, tuberous sclerosis and tetralogy of Fallot

We present a coexistence of cardiac rhabdomyoma, tuberous sclerosis and tetralogy of Fallot. A central shunt was emergently performed because of intractable cyanotic spells. After one-year of follow-up, total correction was performed as regression of the masses along with pulmonary artery growth was achieved. We suggest deferral of surgical total correction until regression of rhabdomyoma masses in these cases.